Ewing Sarcoma of the Kidney: A Rare Entity

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Case Reports in RadiologyVolume 2014 2014, Article ID 283902, 5 pages
Case Report
Diagnostic Radiology Resident, A. C. Camargo Hospital, Sao Paulo, SP, Brazil
Department of Diagnostic Radiology, The University of Texas M. D. Anderson Cancer Center, 1515 Holcombe Boulevard, Houston, TX 77030, USA
Received 26 November 2013; Accepted 19 December 2013; Published 9 January 2014
Academic Editors: C. Chaskis, E. Z. Kapsalaki, and C. Preul
Copyright © 2014 Maria Fernanda Arruda Almeida et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
Abstract
Ewing sarcoma and primitive peripheral neuroectodermal tumor PNET are high-grade malignant tumors typically found in children and adolescents. These tumors belong to the family of small round cell tumors and are of neuroectodermal origin. Primary Ewing sarcoma of the kidney is rare and because of that is an infrequent differential diagnosis in urologic malignancies. Renal PNET mostly presents with nonspecific symptoms such as hematuria and abdominal pain. The imaging findings are uncharacteristic. The diagnosis is based on the histology, immunohistochemistry, and molecular pathologic findings. Once PNET has been diagnosed, multimodal treatment is indicated. Despite all treatment options, the prognosis of those with metastatic disease is poor.
Autor: Maria Fernanda Arruda Almeida, Madhavi Patnana, Brinda Rao Korivi, Neda Kalhor, and Leonardo Marcal
Fuente: https://www.hindawi.com/