An Association of Multiple Well Differentiated Liposarcomas, Lipomatous Tissue and Hereditary RetinoblastomaReportar como inadecuado




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Sarcoma - Volume 9 2005, Issue 3-4, Pages 151-156

Case Report Department of Plastic and Reconstructive Surgery, Royal Devon and Exeter Hospital, Barrack Road, Exeter EX2 5DS, UK



Copyright © 2005 Hindawi Publishing Corporation. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Well differentiated liposarcoma atypical lipomatous tumour is a low grade tumour, with no metastatic potential unlessdedifferentiation supervenes. When superficial, it recurs locally only occasionally after marginal excision. We present apatient in whom bilateral childhood retinoblastoma was followed by later development of massive confluent areas of lowgrade liposarcoma and lipomatous tissue affecting the upper extremities and trunk. We discuss the role of mutations in theretinoblastoma gene RB1 in linking these conditions and demonstrate the surgical management of an extremely unusualand challenging case.





Autor: J. K. O'Neill, C. A. Stone, P. Sarsfield, M. Smith, S. F. Smithson, D. Silver, and V. S. Devaraj

Fuente: https://www.hindawi.com/



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