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Surgical Case Reports

, 2:100

First Online: 21 September 2016Received: 26 July 2016Accepted: 15 September 2016

Abstract

Goodpasture disease GD is a rare autoimmune disorder characterized by the development of pathologic autoantibodies against both glomerular and alveolar basal membranes. Approximately one third of the patients with GD are also positive for anti-neutrophil cytoplasmic antibody ANCA. In this case report, a 74-year-old woman was diagnosed as having myeloperoxidase MPO-ANCA-positive GD with severe aortic valve stenosis AS. She underwent immunosuppressive therapy and plasmapheresis that led to GD remission. Whether a cardiac surgery affects a MPO-ANCA-positive GD in remission is unknown. We reported the outcomes after aortic valve replacement for severe AS in a patient with MPO-ANCA-positive GD.

KeywordsGoodpasture disease MPO-ANCA Interstitial pneumonia  Download fulltext PDF



Autor: Go Kataoka - Ryota Asano - Atsuhiko Sato - Wataru Tatsuishi - Kiyoharu Nakano

Fuente: https://link.springer.com/article/10.1186/s40792-016-0230-x







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