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Pediatric Radiology

, Volume 40, Issue 12, pp 1902–1909

First Online: 03 August 2010Received: 10 May 2010Revised: 25 June 2010Accepted: 06 July 2010

Abstract

BackgroundIntraspinal rib head dislocation is an important but under-recognized consequence of dystrophic scoliosis in patients with neurofibromatosis 1 NF1.

ObjectiveTo present clinical and imaging findings of intraspinal rib head dislocation in NF1.

Materials and methodsWe retrospectively reviewed clinical presentation, imaging, operative reports and post-operative courses in four NF1 patients with intraspinal rib head dislocation and dystrophic scoliosis. We also reviewed 17 cases from the English literature.

ResultsIn each of our four cases of intraspinal rib head dislocation, a single rib head was dislocated on the convex apex of the curve, most often in the mid- to lower thoracic region. Cord compression occurred in half of these patients. Analysis of the literature yielded similar findings. Only three cases in the literature demonstrates the MRI appearance of this entity; most employ CT. All of our cases include both MRI and CT; we review the subtle findings on MRI.

ConclusionAlthough intraspinal rib head dislocation is readily apparent on CT, sometimes MRI is the only cross-sectional imaging performed. It is essential that radiologists become familiar with this entity, as subtle findings have significant implications for surgical management.

KeywordsNeurofibromatosis Dystrophic scoliosis Rib head MRI  Download fulltext PDF



Autor: Jimmy Ton - Rebecca Stein-Wexler - Philip Yen - Munish Gupta

Fuente: https://link.springer.com/







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