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Journal of Medical Case Reports

, 8:77

First Online: 27 February 2014Received: 08 July 2013Accepted: 25 November 2013DOI: 10.1186-1752-1947-8-77

Cite this article as: Shoji, M., Nojima, N., Yoshikawa, A. et al. J Med Case Reports 2014 8: 77. doi:10.1186-1752-1947-8-77


IntroductionCurrarino syndrome Currarino triad was described in 1981 as a triad syndrome with a common embryogenesis in infants and with three characteristics: anorectal stenosis, a defect in the sacral bone, and a presacral mass. We describe here an unusual case of Currarino syndrome in an adult presenting with a presacral abscess but no meningitis.

Case presentationA 32-year-old Japanese man presented with fever, arthralgia and buttock pain. A digital rectal examination showed mild rectal stenosis with local warmth and tenderness in the posterior wall of his rectum. Computed tomography showed a scimitar-shaped deformity of his sacrum and an 8cm presacral mass, which continued to a pedicle of his deformed sacrum. This was diagnosed as Currarino syndrome with a presacral abscess. The abscess was drained by a perianal approach with our patient treated with antibiotics. His symptoms soon disappeared. After three months, an excision was performed through a posterior sagittal approach. His postoperative course was uneventful and he was discharged 10 days after surgery. A histopathological examination revealed an infected epidermoid cyst. He has been free from recurrence as of four years and six months after surgery.

ConclusionsWe report a case of Currarino syndrome in an adult who presented with a presacral abscess but no meningitis. Abscess drainage followed by radical surgery resulted in a successful outcome.

KeywordsAdult Currarino syndrome Epidermal cyst Presacral abscess AbbreviationsCSCurrarino syndrome

CTcomputed tomography

MRImagnetic resonance imaging.

Electronic supplementary materialThe online version of this article doi:10.1186-1752-1947-8-77 contains supplementary material, which is available to authorized users.

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Autor: Masatoshi Shoji - Naomi Nojima - Akemi Yoshikawa - Wataru Fukushima - Naotaka Kadoya - Hisashi Hirosawa - Ryohei Izumi


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