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Journal of Medical Case Reports

, 6:385

First Online: 13 November 2012Received: 04 June 2012Accepted: 05 October 2012DOI: 10.1186-1752-1947-6-385

Cite this article as: Casal, D., Ribeiro, A.I., Mafra, M. et al. J Med Case Reports 2012 6: 385. doi:10.1186-1752-1947-6-385


IntroductionSynovial sarcoma is a high-grade, soft-tissue sarcoma that most frequently is located in the vicinity of joints, tendons or bursae, although it can also be found in extra-articular locations. Most patients with synovial sarcoma of the hand are young and have a poor prognosis, as these tumors are locally aggressive and are associated with a relatively high metastasis rate. According to the literature, local recurrence and-or metastatic disease is found in nearly 80% of patients. Current therapy comprises surgery, systemic and limb perfusion chemotherapy, and radiotherapy. However, the 5-year survival rate is estimated to be only around 27% to 55%. Moreover, most authors agree that synovial sarcoma is one of the most commonly misdiagnosed malignancies of soft tissues because of their slow growing pattern, benign radiographic appearance, ability to change size, and the fact that they may elicit pain similar to that caused by common trauma.

Case presentationWe describe an unusual case of a large synovial sarcoma of the hand in a 63-year-old Caucasian woman followed for 12 years by a multidisciplinary team. In addition, a literature review of the most pertinent aspects of the epidemiology, diagnosis, treatment and prognosis of these patients is presented.

ConclusionAwareness of this rare tumor by anyone dealing with hand pathology can hasten diagnosis, and this, in turn, can potentially increase survival. Therefore, a high index of suspicion for this disease should be kept in mind, particularly when evaluating young people, as they are the most commonly affected group.

KeywordsSynovial sarcoma Hand Surgery Malignant tumor Electronic supplementary materialThe online version of this article doi:10.1186-1752-1947-6-385 contains supplementary material, which is available to authorized users.

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Autor: Diogo Casal - Ana Isabel Ribeiro - Manuela Mafra - Conceição Azeda - Carlos Mavioso - Maria Manuel Mendes - Maria Manue

Fuente: https://link.springer.com/

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