Massive hemoptysis and deep venous thrombosis presenting in a woman with Hughes-Stovin syndrome: a case reportReportar como inadecuado




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Journal of Medical Case Reports

, 4:109

First Online: 21 April 2010Received: 13 January 2009Accepted: 21 April 2010DOI: 10.1186-1752-1947-4-109

Cite this article as: Al-Jahdali, H. J Med Case Reports 2010 4: 109. doi:10.1186-1752-1947-4-109

Abstract

IntroductionHughes-Stovin syndrome is a very rare disease with fewer than 30 cases reported in the literature. The disease is thought to be a variant of Behcet-s disease and is defined by the presence of pulmonary artery aneurysm in association with peripheral venous thrombosis.

Case presentationA previously healthy 23-year-old Saudi woman presented with massive hemoptysis a day prior to her admission to our hospital. She had a six-month history of recurrent fever, cough, dyspnea, and recurrent oral ulceration. Contrast-enhanced computed tomography scan of her chest and pulmonary angiogram demonstrated a single right-lower lobe pulmonary artery aneurysm. She underwent thoracotomy and right lower lobe resection. Her postoperative course was complicated by deep vein thrombosis. She also developed headache and papilledema, while a magnetic resonance imaging of her brain suggested vasculitis. Based on these clinical presentations, she was diagnosed and treated with Hughes-Stovin syndrome.

ConclusionThe majority of cases of Hughes-Stovin syndrome are reported among men, with only two cases occurring in women. A case of Hughes-Stovin syndrome occurring in a woman is presented in this report. She was treated successfully with multimodality treatment that includes surgery, steroids and cytotoxic agents.

Electronic supplementary materialThe online version of this article doi:10.1186-1752-1947-4-109 contains supplementary material, which is available to authorized users.

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Autor: Hamdan Al-Jahdali

Fuente: https://link.springer.com/







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