A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemiaReport as inadecuate




A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia - Download this document for free, or read online. Document in PDF available to download.

Biomarker Research

, 2:7

First Online: 01 April 2014Received: 22 January 2014Accepted: 29 March 2014DOI: 10.1186-2050-7771-2-7

Cite this article as: Tirefort, Y., Pham, XC., Ibrahim, Y.L. et al. Biomark Res 2014 2: 7. doi:10.1186-2050-7771-2-7

Abstract

Primary cutaneous follicle centre lymphoma PCFCL is a rare cutaneous B cell lymphoma in middle-age adults with excellent prognosis. Here we present a case of a patient with a PCFCL in the form of a giant tumour of the scalp in combination with a myeloproliferative neoplasm, JAK2V617F positive essential thrombocythaemia. This case may be of interest because of the favourable outcome in spite of the large size of the PCFCL, the rare combination with essential thrombocythaemia and because it contributes to discussion on the role of JAK2 mutation in such patients.

KeywordsPrimary cutaneous follicle centre lymphoma PCFCL Essential thrombocythaemia JAK2V617F Myeloproliferative neoplasm Electronic supplementary materialThe online version of this article doi:10.1186-2050-7771-2-7 contains supplementary material, which is available to authorized users.

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Author: Yordanka Tirefort - Xuan-Cuong Pham - Yasmine Lucile Ibrahim - Thomas Pierre Lecompte - Thomas Matthes - Christa Prins - B

Source: https://link.springer.com/







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